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来自维基百科,自由的百科全书
肉芽肿并多发性血管炎(Granulomatosis with polyangiitis,缩写GPA),旧称韦格纳肉芽肿(英语:Wegener's granulomatosis,缩写为 WG),又译作华格纳氏肉芽肿,是一种自体免疫疾病,发生原因不明,特征为恶性的血管炎,主要侵犯上、下呼吸道及肾脏,会影响鼻子、肺、肾脏以及其他器官。
肉芽肿并多发性血管炎 Granulomatosis with polyangiitis | |
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同义词 | Wegener's granulomatosis (WG) |
Micrograph showing features characteristic of granulomatosis with polyangiitis – a vasculitis and granulomas with multi-nucleated giant cells. H&E stain. | |
分类和外部资源 | |
医学专科 | 免疫学、风湿病学 |
ICD-11 | 4A44.A1 |
ICD-9-CM | 446.4 |
OMIM | 608710 |
DiseasesDB | 14057 |
MedlinePlus | 000135 |
eMedicine | 332622 |
Orphanet | 900 |
韦格纳肉芽肿初起时的症状为,发生鼻黏膜和肺组织的局灶性肉芽肿性炎症。之后形成血管炎,最终出现弥漫性坏死性肉芽肿性炎症。
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