Senter syndrome

Senter syndrome is a cutaneous condition characterized by similar skin changes and congenital hearing impairment to keratitis–ichthyosis–deafness syndrome, but is associated with glycogen storage leading to hepatomegaly, hepatic cirrhosis, growth failure and intellectual disability.^[2]

Senter syndrome
Other names	Desmons' syndrome[1]
Specialty	Dermatology

See also

• HID syndrome
• List of cutaneous conditions