Tetralogy na Falot
From Wikipedia, the free encyclopedia
Tetralogy na Fallot (TOF) wani nau'in lahani ne na zuciya da ke samuwa a lokacin haihuwa.[1] Alamun a lokacin haihuwa na iya bambanta daga babu zuwa mai tsanani.[2] Daga baya, akwai yawanci lokuta na launin shuɗi zuwa fata da aka sani da cyanosis.[3] Lokacin da jariran da abin ya shafa suka yi kuka ko motsin hanji, za su iya samun “sihiri” inda za su zama shuɗi sosai, suna da wahalar numfashi, su zama rame, wani lokaci kuma su rasa hayyacinsu.[3] Sauran alamomin na iya haɗawa da gunaguni na zuciya, ƙwanƙwasa yatsa, da sauƙin gajiyawa akan shayarwa.[3]
Tetralogy na Falot | |
---|---|
Description (en) | |
Iri |
congenital heart disease (en) , cyanotic heart defect (en) , rare genetic developmental defect during embryogenesis (en) , Ciwon Kwayoyin Halitta, genetic cardiac disease (en) , Trilogy of Fallot (en) cuta |
Specialty (en) |
cardiac surgery (en) pediatrics (en) |
Genetic association (en) | NRP1 (en) , GPC5 (en) , JAG1 (en) , GATA4 (en) , NKX2-5 (en) , ZFPM2 (en) , GATA6 (en) , GDF1 (en) da TBX1 (en) |
Suna saboda | Arthur Fallot (en) |
Medical treatment (en) | |
Magani | alprostadil (en) |
Identifier (en) | |
ICD-10-CM | Q21.3 |
ICD-9-CM | 745.2 |
OMIM | 187500 |
DiseasesDB | 4660 |
MedlinePlus | 001567 |
eMedicine | 001567 |
MeSH | D013771 |
Disease Ontology ID | DOID:6419 |
Yawanci ba a san dalilin ba.[4] Abubuwan haɗari sun haɗa da mahaifiyar da ke amfani da barasa, mai ciwon sukari, ta wuce shekaru 40, ko kamuwa da cutar rubella a lokacin daukar ciki.[4][5] Hakanan ana iya haɗa shi da Down syndrome.[4] A al'adance akwai lahani guda huɗu:[1]
- huhu stenosis, kunkuntar fita daga dama ventricle
- wani lahani na ventricular septal, rami tsakanin ventricles biyu
- ventricular hypertrophy na dama, thickening na dama ventricular tsoka
- Aorta mai wuce gona da iri, wanda ke ba da damar jini daga ventricles biyu don shiga cikin aorta
TOF yawanci ana jinyar ta ta hanyar buɗewar tiyatar zuciya a cikin shekarar farko ta rayuwa.[6] Lokacin tiyata ya dogara da alamun jariri da girmansa.[6] Hanyar ta ƙunshi ƙara girman ƙwayar huhu da jijiyoyi na huhu da gyaran gyare-gyare na ventricular septal.[6] A cikin jariran da suka yi ƙanƙanta, ana iya yin tiyata na wucin gadi tare da tsare-tsare na tiyata na biyu lokacin da jariri ya fi girma.[6] Tare da kulawa mai kyau, yawancin mutanen da abin ya shafa suna rayuwa har su zama manya.[1] Matsalolin na dogon lokaci na iya haɗawa da rashin daidaituwa na bugun zuciya da sakewar huhu.[7]
TOF yana faruwa a kusan 1 cikin 2,000 jarirai.[1] Maza da mata suna shafan daidai.[1] Ita ce mafi yawan hadaddun lahani na cututtukan zuciya wanda ke lissafin kusan kashi 10 na lokuta.[8][9] Niels Stensen ya fara bayyana shi a cikin 1671.[10][11] An buga ƙarin bayanin a cikin 1888 ta likitan Faransa Étienne-Louis Arthur Falot, bayan wanda aka sa masa suna.[10][12] Na farko jimlar gyaran tiyata da aka gudanar a 1954.[7]